Neuronal ceroid lipofuscinosis type 1(CLN1 disease) is a rare autosomal recessive lysosomal storage disease caused by genetic defects of palmitoyl protein thioesterase-1(PPT1). leading to accumulation of lipofuscin granules in brain and progressive neurodegeneration. Psychomotor regression. seizures. https://allfixelectricales.shop/product-category/front-loader-door-catch/